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DSRCT - desmoplastic small round cell tumour

disorder
SNOMED 1156420003CUI C0281508

Overview

DSRCT - desmoplastic small round cell tumour is a disorder. There are currently 3 actively recruiting clinical trials.

Auto-generated from clinical reference data. Not a substitute for medical advice.

Clinical Trials

3
Total Trials
3
Recruiting
1
With Results

Recent Trials

Lurbinectedin in FET-Fused Tumors

NCT05918640Phase 1/PHASE2Recruiting63 enrolled

Phase 1/2 Trial to Evaluate the Safety and Efficacy of PEEL-224 in Combination With Vincristine and Temozolomide in Adolescents and Young Adults With Relapsed or Refractory Sarcomas

NCT06709495Phase 1/PHASE2Recruiting63 enrolled

Therapeutic Trial for Patients With Ewing Sarcoma Family of Tumor and Desmoplastic Small Round Cell Tumors

NCT01946529Phase 2Active Not Recruiting24 enrolled
View all 3 trials on ClinicalTrials.gov

Research Evidence

Peer-reviewed studies linked via MeSH term "Desmoplastic Small Round Cell Tumor" from the MEDLINE/PubMed database.

Sort:
Desmoplastic small round cell tumor: an update of current management practices.
[object Object], [object Object], [object Object] et al. · J Egypt Natl Canc Inst · 2025
PMID: 40254671Review
Desmoplastic Small Round Cell Tumors and the Role of Androgen Receptors.
[object Object], [object Object], [object Object] · Curr Treat Options Oncol · 2025
PMID: 40536706Review
Ewing Sarcoma, Desmoplastic Small Round Cell Tumor, and Other Round Cell Sarcomas.
[object Object], [object Object], [object Object] et al. · Hematol Oncol Clin North Am · 2025
PMID: 40374389ReviewFull text (PMC)
Technical Considerations in Surgical Resection of Desmoplastic Small Round Cell Tumors.
[object Object] · J Pediatr Surg · 2024
PMID: 38368197Review
Abdominopelvic desmoplastic small round cell tumor with metastasis: A case report and literature review.
[object Object], [object Object], [object Object] · Medicine (Baltimore) · 2024
PMID: 38579065ReviewFull text (PMC)
[Pediatric soft tissue tumors : Tumors of uncertain origin].
[object Object], [object Object] · Pathologie (Heidelb) · 2024
PMID: 39356331Review
Effective Treatment of Anlotinib Combined With Chemotherapy in Children With Desmoplastic Small Round Cell Tumor: A Case Series in a Single-center and Literature Review.
[object Object], [object Object], [object Object] et al. · J Pediatr Hematol Oncol · 2024
PMID: 38408140ReviewFull text (PMC)
Desmoplastic Small Round Cell Tumor of the Head and Neck: A Clinicopathological, Immunohistochemical and Molecular Analysis of Three Cases with Literature Review.
[object Object], [object Object], [object Object] et al. · Int J Surg Pathol · 2023
PMID: 36172631Review
Desmoplastic small round cell tumor: from state of the art to future clinical prospects.
[object Object], [object Object], [object Object] et al. · Expert Rev Anticancer Ther · 2023
PMID: 37017324Review
Intra-Abdominal Desmoplastic Small Round Cell Tumor (DSRCT) and the Role of Hyperthermic Intraperitoneal Chemotherapy (HIPEC): A Review.
[object Object], [object Object], [object Object] et al. · Curr Oncol · 2023
PMID: 37185412ReviewFull text (PMC)
Search all PubMed articles for DSRCT - desmoplastic small round cell tumour

Research data from MEDLINE/PubMed

Signs & Symptoms

Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.

Abdominal discomfort
Very frequent (80-99%)HP:0002027
Abnormal peritoneum morphology
Very frequent (80-99%)HP:0002585
Belly bloating
Very frequent (80-99%)HP:0003270
Cancer of connective tissue
Very frequent (80-99%)HP:0100242
Lymph node hyperplasia
Very frequent (80-99%)HP:0002716
Enlarged liver
Frequent (30-79%)HP:0002240
Ileus
Frequent (30-79%)HP:0002595
Nausea and vomiting
Frequent (30-79%)HP:0002017
Swollen lymph nodes in centre of chest
Frequent (30-79%)HP:0100721
Weight loss
Frequent (30-79%)HP:0001824
Ascites
Occasional (5-29%)HP:0001541
Cachexia
Occasional (5-29%)HP:0004326
Cancer of the pancreas
Occasional (5-29%)HP:0002894
Low number of red blood cells or hemoglobin
Occasional (5-29%)HP:0001903
Lung tumor
Occasional (5-29%)HP:0100526
Ovarian neoplasm
Occasional (5-29%)HP:0100615
Testicular cancer
Occasional (5-29%)HP:0010788
Tumors of the central nervous system
Occasional (5-29%)HP:0100006

Related Conditions

Primary desmoplastic small round cell tumor(child)
Sarcoma of soft tissue(parent)

Quick Facts

SNOMED CT
1156420003
UMLS CUI
C0281508
Fully Specified Name
Desmoplastic small round cell tumor (disorder)
Specialists
0
Diagnostic Biomarkers
0
HPO Phenotypes
18
Clinical Trials
3
Medical Disclaimer

This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.

Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.