Treatments & Interventions
Research Evidence
Peer-reviewed studies linked via MeSH term "Idiopathic Pulmonary Fibroses" from the MEDLINE/PubMed database.
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Exposure-Efficacy Meta-Model of Nintedanib in Adult Patients With Chronic Fibrosing Interstitial Lung Diseases.
[object Object], [object Object], [object Object] et al. · CPT Pharmacometrics Syst Pharmacol · 2026
A Systematic Review of Mortality Risk Prediction Models for Idiopathic Pulmonary Fibrosis.
[object Object], [object Object], [object Object] et al. · Br J Hosp Med (Lond) · 2025
PMID: 40265534Meta-Analysis
Transcriptomics of interstitial lung disease: a systematic review and meta-analysis.
[object Object], [object Object], [object Object] et al. · Eur Respir J · 2025
Baseline total lung capacity and all-cause mortality in restrictive pulmonary disorders: a meta-analysis.
[object Object], [object Object], [object Object] et al. · BMC Pulm Med · 2025
Comorbidities in the idiopathic pulmonary fibrosis and progressive pulmonary fibrosis trial population: a systematic review and meta-analysis.
[object Object], [object Object], [object Object] et al. · Eur Respir Rev · 2025
Diagnosis accuracy of machine learning for idiopathic pulmonary fibrosis: a systematic review and meta-analysis.
[object Object], [object Object], [object Object] et al. · Eur J Med Res · 2025
Efficacy and safety of antifibrotic drugs for interstitial lung diseases other than IPF: A systematic review, meta-analysis and trial sequential analysis.
[object Object], [object Object], [object Object] et al. · PLoS One · 2025
Health-related quality of life and health state utility value in idiopathic pulmonary fibrosis: a systematic review and meta-analysis.
[object Object], [object Object], [object Object] et al. · Health Qual Life Outcomes · 2025
Lack of diversity in antifibrotic trials for pulmonary fibrosis: a systematic review.
[object Object], [object Object], [object Object] · Eur Respir Rev · 2025
The 6 Minute Walk Test as a predictor of mortality in idiopathic pulmonary fibrosis: A systematic review.
[object Object], [object Object], [object Object] et al. · Respir Investig · 2025
PMID: 40081204Meta-Analysis
Search all PubMed articles for Idiopathic fibrosing alveolitis
Research data from MEDLINE/PubMed
Signs & Symptoms
Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.
Abnormal lung parenchyma morphology
Very frequent (80-99%)HP:0006530
Bronchiectasis
Frequent (30-79%)HP:0002110
Clubbing of fingers
Frequent (30-79%)HP:0100759
Coughing
Frequent (30-79%)HP:0012735
Decreased DLCO
Frequent (30-79%)HP:0045051
Exertional dyspnea
Frequent (30-79%)HP:0002875
Gastro-esophageal reflux
Frequent (30-79%)HP:0002020
Ground-glass opacification on pulmonary HRCT
Frequent (30-79%)HP:0025179
Honeycombing
Frequent (30-79%)HP:0025175
Persistent blue colour of hands or feet
Frequent (30-79%)HP:0001063
Pulmonary fibrosis
Frequent (30-79%)HP:0002206
Rales
Frequent (30-79%)HP:0030830
Reduced forced vital capacity
Frequent (30-79%)HP:0032341
Reticular pattern on pulmonary HRCT
Frequent (30-79%)HP:0025390
Subpleural honeycombing
Frequent (30-79%)HP:0031631
Tiredness
Frequent (30-79%)HP:0012378
Usual interstitial pneumonia
Frequent (30-79%)HP:0031950
Orthodeoxia
Occasional (5-29%)HP:0033367
Poor exercise tolerance
Occasional (5-29%)HP:0003546
Puolmonary valve insufficiency
Occasional (5-29%)HP:0010444
Alveolar cell carcinoma
HP:0006519
Cirrhosis
HP:0001394
Elevated bronchoalveolar lavage fluid neutrophil proportion
HP:0032977
Hyperglobulinemia
HP:0010702
Panting
HP:0002094
Pulmonary artery hypertension
HP:0002092
Quick Facts
- SNOMED CT
- 700250006
- UMLS CUI
- C1800706
- Fully Specified Name
- Idiopathic pulmonary fibrosis (disorder)
- Specialists
- 0
- Diagnostic Biomarkers
- 0
- HPO Phenotypes
- 26
- Known Treatments
- 2
Medical Disclaimer
This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.
Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.