Overview
Immunoglobulin G4 related aortitis is a disorder.
Auto-generated from clinical reference data. Not a substitute for medical advice.
Signs & Symptoms
Based on Human Phenotype Ontology (HPO) disease-phenotype annotations.
Hypergammaglobulinaemia
Very frequent (80-99%)HP:0010702
Increased circulating IgG4 level
Very frequent (80-99%)HP:0032300
Abdominal discomfort
Frequent (30-79%)HP:0002027
Allergy
Frequent (30-79%)HP:0012393
Antinuclear antibodies
Frequent (30-79%)HP:0003493
Autoimmunity
Frequent (30-79%)HP:0002960
Dilatation of the thoracic aorta
Frequent (30-79%)HP:0012727
Elevated CRP
Frequent (30-79%)HP:0011227
Elevated sedimentation rate
Frequent (30-79%)HP:0003565
High immunoglobulin E
Frequent (30-79%)HP:0003212
Hypereosinophilia
Frequent (30-79%)HP:0032061
Increased inflammatory response
Frequent (30-79%)HP:0012649
Low back pain
Frequent (30-79%)HP:0003419
Pyrexia
Frequent (30-79%)HP:0001945
Reactive airway disease
Frequent (30-79%)HP:0002099
Weight loss
Frequent (30-79%)HP:0001824
Abnormal common carotid artery morphology
Occasional (5-29%)HP:0430021
Abnormality of the aortic arch
Occasional (5-29%)HP:0012303
Anti-neutrophil cytoplasmic antibody positivity
Occasional (5-29%)HP:0032230
Aortic dissection
Occasional (5-29%)HP:0002647
Ascending tubular aorta aneurysm
Occasional (5-29%)HP:0004970
Bowel obstruction
Occasional (5-29%)HP:0005214
Complement deficiency
Occasional (5-29%)HP:0004431
Dilated left subclavian artery
Occasional (5-29%)HP:0031252
Hydronephrosis
Occasional (5-29%)HP:0000126
Quick Facts
- SNOMED CT
- 1187508009
- UMLS CUI
- C5569008
- Fully Specified Name
- Immunoglobulin G4 related aortitis (disorder)
- Specialists
- 0
- Diagnostic Biomarkers
- 0
- HPO Phenotypes
- 25
Medical Disclaimer
This information is for educational purposes only and does not constitute medical advice, diagnosis, or treatment. Always consult with a qualified healthcare provider regarding any medical condition or treatment plan.
Clinical content is derived from the SNOMED CT clinical ontology and curated medical knowledge graphs.